Síndrome de Maffucci e condrossarcoma

Conteúdo do artigo principal

Camila Caetano Solek
Irlena Monica Wisniewska De Moura
Anber Ancel Tanaka
Patricia Martin
João Mario Clementin De Andrade
Vinícius Ferreira Caron
Ricardo Silva dos Santos
Guilherme Nobre Nogueira
Paola Maria Brolin Santis Isolan
Osvaldo Malafaia
Jurandir Marcondes Ribas Filho
Rafaela Fernandes Gonçalves
Gustavo Rassier Isolan

Resumo

Introdução: A síndrome de Maffucci caracteriza-se por múltiplos encondromas subcutâneos e pode ser complicada por condrossarcoma da base do crânio, tumor maligno raro, mas produtor de matriz cartilaginosa que invade a cortical óssea e o tecido medular.


Objetivo: Revisar essa síndrome e sua correlação com condrossarcoma.


Método: Revisão narrativa baseada em informações publicadas com material para leitura e análise selecionado em editoras virtuais, SciELO, BVS - Biblioteca Virtual em Saúde, Pubmed e Scopus. Inicialmente foi realizada busca por descritores relacionados ao tema, existentes no DeCS/MESH utilizando os seguintes termos: “tumor da base do crânio, condrosarcoma, síndrome de Maffucci” e seus correspondentes em inglês com busca AND ou OR, considerando o título e/ou resumo.


Resultado: Após análise dos artigos pertinentes foram selecionados 40 artigos que foram incluídos nesta revisão.


Conclusão: Deve-se ter alto grau de suspeita de lesões da base do crânio em pacientes com síndrome de Maffucci

Detalhes do artigo

Seção
Artigo de Revisão

Referências

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