Síndrome de Maffucci e condrossarcoma
Barra lateral de artigos
Conteúdo do artigo principal
Resumo
Introdução: A síndrome de Maffucci caracteriza-se por múltiplos encondromas subcutâneos e pode ser complicada por condrossarcoma da base do crânio, tumor maligno raro, mas produtor de matriz cartilaginosa que invade a cortical óssea e o tecido medular.
Objetivo: Revisar essa síndrome e sua correlação com condrossarcoma.
Método: Revisão narrativa baseada em informações publicadas com material para leitura e análise selecionado em editoras virtuais, SciELO, BVS - Biblioteca Virtual em Saúde, Pubmed e Scopus. Inicialmente foi realizada busca por descritores relacionados ao tema, existentes no DeCS/MESH utilizando os seguintes termos: “tumor da base do crânio, condrosarcoma, síndrome de Maffucci” e seus correspondentes em inglês com busca AND ou OR, considerando o título e/ou resumo.
Resultado: Após análise dos artigos pertinentes foram selecionados 40 artigos que foram incluídos nesta revisão.
Conclusão: Deve-se ter alto grau de suspeita de lesões da base do crânio em pacientes com síndrome de Maffucci
Detalhes do artigo
Este trabalho está licenciado sob uma licença Creative Commons Attribution 4.0 International License.
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